Primary objectives:
1. Identification of relevant endpoints and outcome measures for clinical trials in STXBP1-RD.
2. Description the longitudinal natural history of patients with STXBP1-RD for external control in interventional studies with disease-modifying therapies.
Secondary objectives:
1. Identification of disease biomarkers in STXBP1-RD (diagnosis, prognosis, treatment effects).
2. Assessment of the disease burden and establish the standard of care of STXBP1-RD.
Natural History Study at a Glance
The NHS will have 50 enrolled participants for the first year of the study. The doctor and caregiver are responsible for entering data.
How does it work?
- in You sign the consent form.
- You and your child:
- come to clinic visit every 3-12 months for assessments
- use the seizure diary app
- fill the questionnaires
- Enter the data:
- You enter the caregiver-reported data.
- Your doctor enters the clinical data.
During the visit at the hospital
The doctor interviews the parents.
The doctor examines the child.
A therapist assesses development.
A technician performs EEG.
A nurse takes a blood test.
The parents answer questionnaires.
A professional Clinical Research Organization (CRO) checks the adherence to the protocol and the quality of data collection at each study site.
